Brazilian Journal of Pulmonology

ISSN (on-line): 1806-3756 | ISSN (printed): 1806-3713

SBPT

Publication continuous and bimonthly

SCImago Journal & Country Rank
Advanced Search

Search Results

The search for the author or contributors found : 3 results


Niemann-Pick disease type B: HRCT assessment of pulmonary involvement

Doença de Niemann-Pick tipo B: avaliação do comprometimento pulmonar por TCAR

Heloisa Maria Pereira Freitas1, Alexandre Dias Mançano2, Rosana Souza Rodrigues1,3, Bruno Hochhegger4, Pedro Paulo Teixeira e Silva Torres5, Dante Escuissato6, Cesar Augusto Araujo Neto7, Edson Marchiori1

J Bras Pneumol.2017;43(6):451-455

Abstract PDF PT PDF EN Portuguese Text

Objective: To analyze HRCT findings in patients with Niemann-Pick disease (NPD) type B, in order to determine the frequency of HRCT patterns and their distribution in the lung parenchyma, as well as the most common clinical characteristics. Methods: We studied 13 patients (3 males and 10 females) aged 5 to 56 years. HRCT images were independently evaluated by two observers, and disagreements were resolved by consensus. The inclusion criteria were presence of abnormal HRCT findings and diagnosis of NPD type B confirmed by histopathological examination of a bone marrow, lung, or liver biopsy specimen. Results: The most common clinical findings were hepatosplenomegaly and mild to moderate dyspnea. The most common HRCT patterns were smooth interlobular septal thickening and ground-glass opacities, which were both present in all patients. Intralobular lines were present in 12 patients (92.3%). A crazy-paving pattern was observed in 5 patients (38.4%), and areas of air trapping were identified in only 1 case (7.6%). Pulmonary involvement was bilateral in all cases, with the most affected area being the lower lung zone. Conclusions: Smooth interlobular septal thickening, with or without associated ground-glass opacities, in patients with hepatosplenomegaly is the most common finding in NPD type B.

 


Keywords: Niemann-Pick diseases; Tomography, X-ray computed; Lung diseases.

 


Pulmonary benign metastasizing leiomyoma presenting as small, diffuse nodules

Leiomioma metastático benigno pulmonar apresentando padrão de pequenos nódulos difusos

Jean-Michel Dossegger1,a, Leonardo Hoehl Carneiro1,b, Rosana Souza Rodrigues1,2,c, Miriam Menna Barreto1,d, Edson Marchiori1,e

J Bras Pneumol.2019;45(4):e20180318-e20180318

PDF PT PDF EN Portuguese Text



Diffuse pulmonary lymphangiomatosis

Linfangiomatose pulmonar difusa

Igor Biscotto1,a, Rosana Souza Rodrigues1,2,b, Danielle Nunes Forny1,c, Miriam Menna Barreto1,d, Edson Marchiori1,e

J Bras Pneumol.2019;45(5):e20180412-e20180412

PDF PT PDF EN Portuguese Text



 

 


The Brazilian Journal of Pulmonology is indexed in:

Latindex Lilacs SciELO PubMed ISI Scopus Copernicus pmc

Support

CNPq, Capes, Ministério da Educação, Ministério da Ciência e Tecnologia, Governo Federal, Brasil, País Rico é País sem Pobreza
Secretariat of the Brazilian Journal of Pulmonology
SCS Quadra 01, Bloco K, Salas 203/204 Ed. Denasa. CEP: 70.398-900 - Brasília - DF
Fone/fax: 0800 61 6218/ (55) (61) 3245 1030/ (55) (61) 3245 6218
E-mails: jbp@jbp.org.br
jpneumo@jornaldepneumologia.com.br

Copyright 2019 - Brazilian Thoracic Association

Logo GN1